What is it?

Bronchopulmonary sequestration (BPS) is a congenital malformation of the lower respiratory tract in which a portion of the lung develops without connection to the normal airways. It also has an abnormal blood supply derived from the aorta.

How common is it?

BPS is a rare condition, comprising less than 5% of all congenital lung abnormalities.

How is it managed?

If suspected upon ultrasound, an MRI can be obtained in order to differentiate BPS from other chest conditions. Serial ultrasounds are performed throughout the pregnancy, as the lesion may increase in size, remain stable, or regress. Magnetic resonance imaging (MRI) is also recommended to better define these lesions, and fetal echocardiography is also performed to exclude associated heart problems. Consultations with neonatology and pediatric surgery are recommended to discuss prognosis and management after birth.

Postnatal/Prognosis?

After delivery, chest imaging studies are recommended and some symptomatic newborns may require surgery. In the absence of other anomalies, most cases of BPS detected before delivery have an excellent outcome.